Abstract:Objecitve To elucidate the clinical problems, diagnosis and treatment of primary appendiceal adenocarcinoma. Methods A case of primary appendiceal adenocarcinoma was analyzed retrospectively, and its literature at home and abroad was reviewed. Results The patient was admitted to the hospital with acute appendicitis and was confirmed as appendiceal adenocarcinoma by postoperative pathological diagnosis.No recurrence or discomfort occurred during half a year of follow-up. Conclusion Primary adenocarcinoma of the appendix is rare and should be paid more attention in clinic.Rapid pathological assessment and right hemicolectomy during operation can improve the prognosis of patients.